Ganglioneuroma presenting as an adrenal incidentaloma: A case report

  • Nguyen Thi Thuy 108 Military Central Hospital
  • Luu Thuy Quynh 108 Military Central Hospital
  • Vu Thi Loan 108 Military Central Hospital
  • Nguyen Van Manh 108 Military Central Hospital
  • Ngo Thi Phuong 108 Military Central Hospital
  • Ngo Quan Vu 108 Military Central Hospital

Main Article Content

Keywords

Ganglioneuroma, adrenal incidentaloma

Abstract

Ganglioneuromas (GNs), benign tumors of sympathetic neuvous systems arising from the neural crest tissue and are most commonly located in the posterior mediastinum and retroperitoneum. They are rarely found in the adrenal gland, asymptomatic and incidentaloma in almost cases. Although GNs is benign but it can grow and cause compression, so surgery is the optimal treatment method. It is complicated to diagnose exactly before surgering, difficult distinction with adrenal cortical carcinoma. Postoperatively, there is no need for adjuvant therapy in patients with adrenal GNs and their progonist is excellent. We report the clinical case describing adrenal ganglioneuroma, without exact diagnosis and the exception of adrenal cortical carcinoma. Postoperation, the patient has a good recover. Histopathological examination is required in order to confirm the diagnosis of GNs. Conclusion: Adrenal ganglioneuroma is benign, occurs rarely and preoperative diagnosis is difficult, thus surgery is the gold standard for the treatment and histopathological examination is the mainstay of diagnosis.

Article Details

References

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