Leiomyoma arising from Mullerian remnant in a patient with Mayer-Rokitansky-Küster-Hauser syndrome: A case report and literature review

  • Hoàng Thị Tùng Anh Bệnh viện Trung ương Quân đội 108
  • Nguyễn Thanh Hà Bệnh viện Trung ương Quân đội 108
  • Lê Văn Tuyên Bệnh viện Trung ương Quân đội 108
  • Lê Khắc Duy Bệnh viện Trung ương Quân đội 108
  • Phạm Hoàn Mỹ Đại học VinUniversity

Main Article Content

Keywords

Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome, leiomyoma, Mullerian remnant

Abstract

Objective: To report a case of leiomyoma arising from Mullerian remnant in a patient with Mayer-Rokitansky-Küster-Hauser (MRKH) Syndrome at 108 Military Central Hospital, and to review studies on diagnosis and treatment of this disease. Case report: A 48-year-old female, with past medical history of MRKH syndrome, presented with hypogastric pain. Ultrasonography and abdominal CT scan showed a pelvic mass, suspecting an ovarian tumor. The patient was performed laparoscopy to find out the tumor on Mullerian remnant. The tumor was resected. Pathology confirmed leiomyoma. Postoperative period was uneventful. No other intervention was required. Conclusion: Leiomyoma in patients with MRKH syndrome is a rare finding. Laparoscopy is a helpful diagnostic and therapeutic modality. Tumor resection on mullerian remanant is indicated if the patient is symptomatic.

Article Details

References

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Published
Dec 30, 2024
DOI: https://doi.org/10.52389/ydls.v19i8.2492
Issue
Volume 19-No 8/2024
Section
Articles
How to Cite
AnhH. T. T., HàN. T., TuyênL. V., DuyL. K., & MỹP. H. (2024). Leiomyoma arising from Mullerian remnant in a patient with Mayer-Rokitansky-Küster-Hauser syndrome: A case report and literature review. Tạp Chí Y Dược lâm sàng 108, 19(8). https://doi.org/10.52389/ydls.v19i8.2492