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Abstract

Pulmonary Sclerosing Pneumocytoma (PSP), formerly known as sclerosing pulmonary hemangioma, is a rare lung tumor first described in 1956 by Liebow et al showed marked fibrosis and vascular proliferation. PSP has been shown to be of epithelial origin, most likely from type II alveolar cells. The basic feature of PSP is the presence of cuboidal surface cells and circular stromal cells, both of which are thought to be neoplastic. In the 2015 World Health Organization (WHO) classification (updated 2021), “multiple/mixed tumors” were changed to “adenomas” and PSP to be classified as adenomas. In this classification, lung adenomas include: (1) Sclerosing Pneumocytoma; (2) Alveolar adenoma; (3) Papillary Adenoma; (4) Bronchiolar adenoma/Ciliated muconodular papillary tumour; (5) Mucinous Cystadenoma; (6) Mucinous gland adenoma.              Most PSPs are benign, with very rare possibility of malignancy. On radiographs and computed tomography (CT) scans, tumors often present as solitary nodules, are often discovered incidentally, and patients are often asymptomatic. The problem of differential diagnosis, confirmed benign is still a challenge for experts. We introduce the case of a 67-year-old male patient who came to the National Lung Hospital for examination and treatment, was diagnosed with PSP by histopathology and retrospectively related documents for colleagues to consult.